Left Ventricular Noncompaction

  • R Malla Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • Ranjit Sharma Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • B Rauniyar Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • M B KC Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • A Maskey Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • D Joshi Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu
  • S Hamal Department of Cardiology, Shahid Gangalal National Heart Center, Bansbari, Kathmandu

Abstract

Left Ventricular Noncompaction(LVNC) is a genetic cardiac disease of emerging importance with
a distinct clinical and pathophysiological presentation. The most common clinical manifestations
include heart failure,arrhythmias and embolic events, and in children it may be associatedwith
facial dysmorphisms and Wolff–Parkinson–Whitesyndrome. The diagnosis of LVNC, however,
is often missed, most often as a consequence of ignorance of the condition. Echocardiography is
considered the reference standard for the diagnosis of LVNC. Prognosis remains poor for patients
with impaired systolic left ventricular function, as treatment options are very limited. Because of the
familial association of LVNC, fi rst-degree relatives should be screened by Echocardiography.
Key Words: heart, left ventricle, noncompaction

Published
2009-04-01
How to Cite
Malla, R., Sharma, R., Rauniyar, B., KC, M. B., Maskey, A., Joshi, D., & Hamal, S. (2009). Left Ventricular Noncompaction. Journal of Nepal Medical Association, 48(174), 180-4. https://doi.org/10.31729/jnma.241
Section
Review Article