Left Ventricular Noncompaction
Left Ventricular Noncompaction(LVNC) is a genetic cardiac disease of emerging importance with
a distinct clinical and pathophysiological presentation. The most common clinical manifestations
include heart failure,arrhythmias and embolic events, and in children it may be associatedwith
facial dysmorphisms and Wolff–Parkinson–Whitesyndrome. The diagnosis of LVNC, however,
is often missed, most often as a consequence of ignorance of the condition. Echocardiography is
considered the reference standard for the diagnosis of LVNC. Prognosis remains poor for patients
with impaired systolic left ventricular function, as treatment options are very limited. Because of the
familial association of LVNC, fi rst-degree relatives should be screened by Echocardiography.
Key Words: heart, left ventricle, noncompaction
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