Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report

Authors

DOI:

https://doi.org/10.31729/jnma.7019

Keywords:

juvenile arthritis; macrophage activation syndrome; steroids.

Abstract

Macrophage activation syndrome is a rare but a life threatening condition commonly associated with Systemic Juvenile Idiopathic Arthritis. Its clinical presentation includes fever, hepatosplenomegaly, hypertriglyceridemia, hypofibrinogenemia, hyperferritinemia and impaired liver enzymes. The symptoms are alarming yet non-specific and often lead to a delayed diagnosis. A 12 year male presented with a history of intermittent fever and was started on antibiotics but failed to respond after several days of hospital stay. After a series of investigations to rule out multiple diagnoses he was diagnosed as a case of Macrophage Activation Syndrome secondary to Systemic onset Juvenile Arthritis and was treated with steroids.

Additional Files

Published

2021-11-15

How to Cite

Kafle, R. ., Bhatta, A. ., Gami, S. ., Sapkota, A., Sharma, D., Yadav, A., & Chikanbanjar, V. K. (2021). Macrophage Activation Syndrome secondary to Systemic Juvenile Idiopathic Arthritis: A Case Report. Journal of Nepal Medical Association, 59(243), 1166–1169. https://doi.org/10.31729/jnma.7019

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