Fontan Failure and Thrombosis of Total Cavo-Pulmonary Connection Conduit

Authors

  • Nirmal Panthee Department of Cardiac Surgery, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan.
  • Arata Murakami Department of Cardiac Surgery, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan.
  • Masahiko Ando Department of Cardiac Surgery, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan.
  • Tetsuhiro Takaoka Department of Cardiac Surgery, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan
  • Minoru Ono Department of Cardiac Surgery, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113-8655, Japan.

DOI:

https://doi.org/10.31729/jnma.2762

Keywords:

congenital heart disease; fontan procedure; thrombosis.

Abstract

The immediate postoperative period of Fontan operation is frequently complicated by hemodynamic instability, sometimes requiring fenestration of the conduit. Thrombosis of total cavo-pulmonary connection conduit warrants early intervention to prevent systemic and pulmonary embolism. We report a case of Fontan failure requiring fenestration; which was further complicated by thrombosis of total cavo-pulmonary connection conduit and managed with anticoagulants. 

Keywords: congenital heart disease; fontan procedure; thrombosis.

References

Anderson BW, Barron DJ, Jones TJ, Edwards L, Brawn W,
Stumper O. Catheter takedown in the management of the
acutely failing Fontan circulation. Ann ThoracSurg. 2011
Jul;92(1):346-8.
2. Rychik J, Goldberg D, Dodds K. Long-term results
and consequences of single ventricle palliation.
ProgPediatrCardiol. 2010 May;29(1):19-23.
3. Shirai LK, Rosenthal DN, Reitz BA, Robbins RC, Dubin AM.
Arrhythmias and thromboembolic complications after the
extracardiac Fontan operation. J Thorac Cardiovasc Surg.
1998 March;115(3):499-505.
4. Rosenthal DN, Friedman AH, Kleinman CS, Kopf GS,
Rosenfeld LE, Hellenbrand WE. Thromboembolic
complications after Fontan operations.Circulation.
1995;92:287-93.
5. Marrone C, Galasso G, Piccolo R, deLeva F, Paladini R,
Piscione F, et al. Antiplatelet versus anticoagulation therapy
after extracardiac conduit Fontan: A systematic review and
meta-analysis. Pediatr Cardiol. 2011 Jan;32(1):32-9.
6. Kim SJ, Kim WH, Lim HG, Lee JY. Outcome of 200 patients
after an extracardiac Fontan procedure. J Thorac Cardiovasc
Surg. 2008 Jul;136(1):108-16.
7. Kreutzer C, Schlichter AJ, Simon JL, Conejeros Parodi
WM, Blunda C, Kreutzer GO. A new method for reliable
fenestration in extracardiac conduit Fontan operations. Ann
Thorac Surg. 2003 May;75(5):1657-9.
8. Konstantinov IE, Puga FJ, Alexi-Meskishvili VV. Thrombosis
of intracardiac or extracardiac conduits after modified Fontan
operation in patients with azygous continuation of the
inferior vena cava. Ann Thorac Surg. 2001 Nov;72(5):1641-4.
9. Rauch R, Sieverding L, Hofbeck M. Thrombosis of an
extracardiac Fontan tunnel: Combined treatment of
thrombolysis and stenting. Catheter Cardiovasc Interv. 2009
Nov;74(6):917-9.

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How to Cite

Panthee, N., Murakami, A., Ando, M., Takaoka, T., & Ono, M. (2014). Fontan Failure and Thrombosis of Total Cavo-Pulmonary Connection Conduit. Journal of Nepal Medical Association, 52(194), 834–836. https://doi.org/10.31729/jnma.2762

Issue

Vol. 52 No. 194 (2014)

Section

Case Reports

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