Panniculitis in Anti-MDA-5 Positive Juvenile Dermatomyositis: A Case Report

Authors

  • Semra Ayduran Department of Pediatric Rheumatology, Pamukkale University, Denizli, Turkiye
  • Gulsah Kilbas Department of Pediatric Rheumatology, Pamukkale University, Denizli, Turkiye
  • Saadet Nilay Tigrak Department of Pediatric Rheumatology, Pamukkale University, Denizli, Turkiye
  • Selcuk Yuksel Department of Pediatric Rheumatology, Canakkale Onsekiz Mart University, Canakkale, Turkiye
  • Erdem Comut Department of Pathology, Pamukkale University, Pathology, Denizli, Turkiye
  • Serkan Turkucar Department of Pediatric Rheumatology, Pamukkale University, Denizli, Turkiye

DOI:

https://doi.org/10.31729/jnma.8874

Keywords:

anti MDA-5, dermatomyositis, panniculitis

Abstract

Panniculitis is a rare clinical finding in dermatomyositis. There are few reported cases in the medical literature. In this report, we describe a 17-year-old male patient with anti-MDA5 positive hypomyopathic dermatomyositis who, eight months after diagnosis, presented with indurated nodules on the right forearm and right thigh despite methotrexate and monthly intravenous immunoglobulin treatment. A skin biopsy revealed lobular panniculitis with lymphocytic infiltrate. His lesions were successfully controlled with hydroxychloroquine and azathioprine. This article presents a case regarding the rarity of panniculitis in juvenile dermatomyositis and its treatment strategy.

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Published

2024-12-31

How to Cite

Ayduran, S., Kilbas, G., Tigrak, S. N., Yuksel, S., Comut, E., & Turkucar, S. (2024). Panniculitis in Anti-MDA-5 Positive Juvenile Dermatomyositis: A Case Report. Journal of Nepal Medical Association, 63(281), 61–64. https://doi.org/10.31729/jnma.8874